RT Journal Article
SR Electronic
T1 Cardiac conduction abnormalities and Stokes-Adams attacks in myotonic dystrophy
JF Canadian Medical Association Journal
JO CMAJ
FD Canadian Medical Association
SP 1402
OP 1404
VO 118
IS 11
A1 Noel, C.
A1 Gagnon, R. M.
YR 1978
UL http://www.cmaj.ca/content/118/11/1402.abstract
AB Myotonic dystrophy is a well known cause of cardiomyopathy. While various cardiac conduction abnormalities have been described in patients with myotonic dystrophy, so far only sporadic cases of Stokes-Adams attacks have been reported. Of 27 patients with this disease various conduction disturbances were detected in 17 (63%), 5 of whom presented with Stokes-Adams attacks and were found to have intracardiac conduction defects. The prognosis in four of the five patients was greatly improved with permanent pacemaker implantation.